Marfan Syndrome: Aortic Root Surgery

Marfan Syndrome

Aortic Repair

This is a 30-year old male patient with Marfan syndrome who was followed by his cardiologist for a dilated aortic root aneurysm. The patient's father and 2 of 4 siblings also have Marfan syndrome. One of his sisters suffered a Type A aortic dissection. The patient's aortic root aneurysm was 5 cm and echocardiogram indicated mild aortic valve insufficiency. The diameter of the distal segment of the ascending aorta was normal. An aortic valve-sparing root replacement was offered to the patient. A 32-mm graft was used to replace the aortic root. The patient's post-operative course was uneventful and echocardiogram indicated no aortic valve insufficiency. 

Please enjoy the abbreviated version of the surgical video: